CFTR, Growth & Liver Disease: A Clinical Perspective


Take our post-test to claim CME credits.

To read a companion newsletter click here.

Where, beyond the lungs, do CFTR modulators provide beneficial effects? Can treatment promote growth in height and BMI? What’s known about CFTR modulator effects on cystic fibrosis-associated liver disease?  

In this eCysticFibrosis Review podcast, Drs. Darla Shores and Anna Reed from the THRIVE Pediatric Intestinal Rehabilitation Center in the Division of Gastroenterology, Hepatology, and Nutrition at the Johns Hopkins Children’s Center take us to the clinic to answer these and other questions crucial to the health of our patients with cystic fibrosis. 

In the Clinic: Triple Combination CFTR Modulation

Take our post-test to claim CME credits.

To read a companion newsletter click here.

Elexacaftor/tezacaftor/ivacaftor — the newly approved triple combination CFTR modulator therapy.  What are the benefits?  For which patients?  What are the potential adverse effects?  Who’s most likely to receive them?  

In this issue, Dr. Scott Sagel from the Breathing Institute at the Children’s Hospital Colorado, part of the University of Colorado’s Anschutz Medical Campus, takes us to the clinic to discuss some answers. 

In The Clinic: CFTR Modification & Nutritional Deficiencies

Volume 8, Issue 9.

In this issue:

The effects of CFTR modifiers on improving lung function in people with cystic fibrosis are well known. But what about their effects on the GI tract that directly affect nutrition?

In this issue, Dr. Michael Wilschanski — Director of Hadassah Hospital’s Pediatric Gastroenterology Unit at Hebrew University in Jerusalem — explains how new findings about CFTR modification can impact clinical practice.

Take our post-test to claim CME credits.

To read a companion newsletter click here.

Clinical Insight: CFTR Modulators

Volume 8, Issue 6.

In this issue, Dr. Gregory Sawicki — Associate Professor of Pediatrics at Harvard Medical School and Director of the Cystic Fibrosis Center at Boston Children’s Hospital — discusses how the recent findings about the real-world use of CFTR modulators can impact clinical practice.

Take our post-test to claim CME credits.

To read a companion newsletter click here.

CFTR Modulators: Clinical Insights

Volume 7, Issue 12.

In this podcast Dr. John P. Clancy reviews CFTR modulators, and discusses insights presented at the 2017 NACFC.

Take our post-test to claim CME credits:
Physician post-test
Nurse post-test

To read a companion newsletter click here.

New Directions in CFTR Modification

Volume 7, Issue 8.

In this podcast Dr. George Solomon discusses new directions in CFTR modification in the context of case studies.

Take our post-test to claim CME credits:
Physician post-test
Nurse post-test

To read a companion newsletter click here.

Future Landscape of CFTR Modulators

Volume 6, Issue 12.

Claire Wainwright, FRACP, MD and Tonia Douglas, MD cover the important topic of the Future Landscape of CFTR Modulators in the format of case-study scenarios for the clinical practice.

Take our post-test to claim CME credits:
Physician post-test
Nurse post-test

To read a companion newsletter click here.

Pseudomonas aeruginosa Eradication and Outcomes: Key Questions

Volume 6, Issue 10.

Christopher Oermann, MD covers the important topic of the Pseudomonas Eradication in the format of case-study scenarios for the clinical practice.

Take our post-test to claim CME credits:
Physician post-test
Nurse post-test

To read a companion newsletter click here.

Nutritional Issues in Cystic Fibrosis

Volume 6, Issue 8.

Dr. Deepak Agrawal, MD covers the important topic of Nutritional Issues in Cystic Fibrosis in the format of case-study scenarios for the clinical practice.

Take our post-test to claim CME credits:
Physician post-test
Nurse post-test

To read a companion newsletter click here.

Trends in Inhaled Antibiotic Therapy

Volume 6, Issue 6.

Daniel Heintz, MD and Karen McCoy, MD cover the important topic of Trends in Inhaled Antibiotic Therapy in the format of case-study scenarios for the clinical practice.

Take our post-test to claim CME credits:
Physician post-test
Nurse post-test

To read a companion newsletter click here.