Highlights of the 27th Annual North American Cystic Fibrosis Conference

Special Edition 2014 – Kenneth Olivier.

In this special edition of eCystic Fibrosis review, Dr. Peter Mogayzel discusses highlights from Dr. Kenneth Olivier’s talk on Nontuberculosis Mycobacteria: Updates in CF presented at the 27th Annual North American Cystic Fibrosis Conference in Salt Lake City, Utah.

New Therapies in Cystic Fibrosis Directed Toward the Basic Defect

Volume 4, Issue 8.

In this podcast guest author Steven Rowe, MD, Associate Professor of Medicine from the University of Alabama at Birmingham, describes how CFTR modulator therapy fits into the clinical armamentarium of CF lung disease; identifies which patients are most appropriate for CF modulator treatment; and describes current research efforts and how to identify patients suitable for referral for consideration in CFTR modulator clinical trials.

P. aeruginosa Eradication

Volume 4, Issue 6.

In this podcast guest author Dr. Margaret Rosenfeld from the University of Washington School of Medicine, discusses the rationale for early Pseudomonas aeruginosa eradication, Identifies the inhaled and oral antibiotics that have been compared in clinical trials for early Pseudomonas eradication, and describes the potential adverse effects of early Pseudomonas eradication therapy.

Strategies for the Improvement of Nutrition Outcomes

Volume 4, Issue 4.

In this podcast guest author Amanda Radmer Leonard, Pediatric Nutrition Practitioner, of the Johns Hopkins Children’s Center, describes approaches to the treatment of low vitamin D levels in patients with cystic fibrosis, discuss the variability of fecal elastase result during the first year of life, and summarizes the importance of tailoring nutritional interventions to specific patient and family situations.

Adherence to Chronic Inhaled Therapies

Volume 4, Issue 2.

Nonadherence to any medical regimen is common particularly among adolescents and young adults, and cystic fibrosis (CF) is no exception. There are many barriers to following the complex daily regimen that CF management requires, and researchers and clinicians have not yet found the ideal approach for counseling and supporting patients to improve and maintain their level of adherence. In this podcast Dr. Kristin Riekert, of The Johns Hopkins Adherence Research Center discusses best practices for determining which clinic patients are nonadherent and Identifies risk factors for nonadherence.

Featured Cases: Emerging Pathogens in Cystic Fibrosis

Volume 3, Issue 12.

Case studies offer opportunity to differentiate the needs of each patient when managing respiratory infections. Dr. Elliott Dasenbrook will review the prevalence of important CF organisms over the last 10 years, the impact of respiratory tract MRSA on survival, the association between a virulent strain of P. aeruginosa that can spread among patients and lung transplant or death, as well as the impact of chronic non-tuberculous Mycobacterial lung disease on lung function.

Featured Cases: The Role of Exercise and Physical Activity in Optimizing Outcomes Among Patients with CF

Volume 3, Issue 10.

Dr. Elizabeth Yen offers a clinical perspective to her review on how new research that highlights the strong positive impact of early behavioral and nutritional education and predictors of long-term response to such interventions. In this podcast she will expand on that information by discussing case scenarios.

Featured Cases: Interventions to Improve Nutrition in Patients with CF

Volume 3, Issue 8.

In this issue, Dr. Elizabeth Yen reviews new research highlighting the strong positive impact of early behavioral and nutritional education. Exploring predictors of long-term response to such interventions she discusss how body image may affect compliance with nutritional recommendations in adolescents; and, then present data describing positive outcomes with gastrostomy tube placement for supplemental enteral intake.

Featured Cases: Exacerbation Therapies

Volume 3, Issue 4.

This podcast has been developed for clinicians caring for patients with issues related to cystic fibrosis. You can also read the companion newsletter. In this edition Dr. Chris Goss will explain the use of new inhalation therapies for the treatment of cystic fibrosis, with the discussion some typical case scenarios.